A rare case of a neonate with fallot-type absent pulmonary valve and occlusion of the left main bronchus

J Cardiothorac Surg. 2024 Feb 6;19(1):61. doi: 10.1186/s13019-024-02534-z.


Fallot-type absent pulmonary valve is a rare and complex congenital heart disease. Repair surgery for this condition during the neonatal period has a mortality rate of over 50%. We reported a neonate with Fallot-type absent pulmonary valve and occlusion of the left main bronchus. The patient's pulmonary artery had unusual anatomy of a type that has not previously been reported. This case report outlines a successful treatment strategy for patients with complex congenital heart disease and airway occlusion during the neonatal period and the effect of these unusual anatomical conditions on postoperative outcomes.

Keywords: Absent pulmonary valve; Occlusion of the left main bronchus; Tetralogy of Fallot.

Publication types

  • Case Reports

MeSH terms

  • Bronchi
  • Humans
  • Infant, Newborn
  • Pulmonary Artery / surgery
  • Pulmonary Atresia*
  • Pulmonary Valve* / surgery
  • Tetralogy of Fallot* / surgery