IgG4-related disease presenting with acute kidney injury and tubulointerstitial nephritis

Proc (Bayl Univ Med Cent). 2024 Feb 8;37(2):319-321. doi: 10.1080/08998280.2023.2288470. eCollection 2024.


Immunoglobulin G-4 related disease (IgG4-RD) is an immune-mediated, inflammatory disease that often involves multiple organ systems. IgG4-RD can be classified according to the organs involved. Type 1 IgG4-RD is related to acute pancreatitis and sclerosing cholangitis. Disease manifestation is also seen in the retroperitoneal region, pelvic organs, and orbital space. Here we describe a rare case of IgG4-RD causing isolated acute kidney injury.

Keywords: Acute kidney injury; IgG4-related disease; hemodialysis; uremia.

Publication types

  • Case Reports