Medical Therapy and Monitoring in Adult Congenital Heart Disease Heart Failure

Heart Fail Clin. 2024 Apr;20(2):137-146. doi: 10.1016/j.hfc.2023.12.002. Epub 2023 Dec 29.


Heart failure (HF) in adult congenital heart disease (ACHD) is an increasingly common problem facing ACHD and advanced heart disease and transplant providers. Patients are highly nuanced, and therapies are poorly studied. Standard HF medications are often used in patients who are not targets of large clinical trials. HF management in this data-free zone requires focused, comprehensive team-based care and close follow-up and communication with patients.

Keywords: Adult congenital heart disease; Eisenmenger syndrome; Follow-up; Fontan; Heart failure; Heart failure therapies; Systemic right ventricle.

Publication types

  • Review

MeSH terms

  • Adult
  • Heart
  • Heart Defects, Congenital* / complications
  • Heart Defects, Congenital* / therapy
  • Heart Failure* / therapy
  • Humans