An Unusual Presentation of Double-Outlet Right Atrium

World J Pediatr Congenit Heart Surg. 2024 Apr 26:21501351241237956. doi: 10.1177/21501351241237956. Online ahead of print.

Abstract

We describe an unusual example of double-outlet right atrium with separate atrioventricular junctions. The straddling and overriding tricuspid valve had two orifices, and the mitral valve was morphologically normal. An appropriate understanding of the morphology of the atrioventricular junctions, the valves, and the subvalvar apparatus, along with the location of the atrioventricular conduction axis, allowed for successful biventricular repair.