A Variant of Gorlin-Goltz Syndrome with Synchronous Malignant and Multiple Benign Lesions of the Jaws - A Case Report

Indian J Dent Res. 2023 Oct 1;34(4):451-454. doi: 10.4103/ijdr.ijdr_9_23. Epub 2024 Apr 19.

Abstract

Introduction: Although numerous syndromic and non-syndromic odontogenic lesions of the jaws have been documented in the literature, there are very few cases of simultaneous benign and malignant jaw lesions.

Patient concerns: We present a case of right maxillary squamous cell carcinoma along with several benign odontogenic cystic lesions of the jaws and skeletal abnormalities that meet the criteria for Gorlin-Goltz syndrome.

Takeaway lessons: With a review of the literature, the specifics of management and follow-up are discussed.

Publication types

  • Case Reports

MeSH terms

  • Basal Cell Nevus Syndrome* / complications
  • Basal Cell Nevus Syndrome* / pathology
  • Carcinoma, Squamous Cell / pathology
  • Female
  • Humans
  • Male
  • Maxillary Neoplasms* / diagnostic imaging
  • Maxillary Neoplasms* / pathology
  • Neoplasms, Multiple Primary / diagnostic imaging
  • Neoplasms, Multiple Primary / pathology
  • Odontogenic Cysts* / diagnostic imaging
  • Odontogenic Cysts* / pathology
  • Radiography, Panoramic