The large vestibular aqueduct syndrome

Am J Otol. 1985 Sep;6(5):387-415.


The hypocycloidal polytomographic temporal bone studies performed on 2683 patients were reviewed, and the radiographic appearance of the vestibular aqueduct was evaluated. Within this group of 5366 ears, forty-seven ears (1%) in twenty-six patients demonstrated a large vestibular aqueduct (diameter greater than 1.5 mm). A review of the relevant embryology, anatomy, and physiology is reported. A discussion of hypocycloidal polytomography and computed tomography of the temporal bone as well as a discussion of the Mondini dysplasia is also presented. The twenty-six patients underwent a battery of audiometric and vestibular function tests. These data were compiled and correlations made, allowing for a more complete characterization of the large vestibular aqueduct syndrome.

MeSH terms

  • Adolescent
  • Adult
  • Audiometry
  • Audiometry, Evoked Response
  • Child
  • Child, Preschool
  • Electronystagmography
  • Evoked Potentials, Auditory
  • Female
  • Humans
  • Labyrinth Diseases / diagnosis
  • Labyrinth Diseases / diagnostic imaging*
  • Male
  • Syndrome
  • Tomography, X-Ray Computed
  • Vestibular Aqueduct / abnormalities
  • Vestibular Aqueduct / diagnostic imaging*
  • Vestibular Function Tests
  • Vestibule, Labyrinth / diagnostic imaging*