Cushing Syndrome Is Associated With a Higher Risk of Cancer-A Nationwide Cohort Study

J Clin Endocrinol Metab. 2025 Apr 22;110(5):1419-1426. doi: 10.1210/clinem/dgae405.

Abstract

Context: Patients with Cushing syndrome (CS) have higher risk of obesity and diabetes, which are important risk factors of cancers. However, if patients with CS have a higher incidence of cancer remains unknown.

Objective: To investigate whether endogenous CS is associated with increased cancer incidence.

Methods: A nationwide cohort study analyzing data retrieved from Taiwan's National Health Insurance program in 2006-2017. Between 2006 and 2017, 1278 patients with newly diagnosed endogenous CS were identified. Among them, 1246 patients without a history of malignancy were enrolled in this study. The age- and sex-standardized incidence rate of all-cause cancer and age-, sex-, and calendar year-standardized incidence ratio (SIR) of cancer in association with endogenous CS.

Results: The age- and sex-standardized incidences of CS decreased from 4.84 to 3.77 per million person-years between 2006 and 2017. The age at diagnosis of CS was 45.3 ± 14.8 years, and 80.0% of the patients were female. Cushing disease and adrenal CS accounted for 35.4% and 64.6% of patients with CS, respectively. The incidence rate of cancer in patients with CS was 7.77 (95% CI 5.84-10.14) per 1000 person-years, with a SIR of 2.08 (95% CI 1.54-2.75). The 3 most common cancer types were liver (27.7%), kidney (16.7%), and lung (13.0%).

Conclusion: Patients with endogenous CS have a higher incidence of cancer.

Keywords: Cushing syndrome; cancer risk; incidence.

MeSH terms

  • Adult
  • Aged
  • Cohort Studies
  • Cushing Syndrome* / complications
  • Cushing Syndrome* / epidemiology
  • Female
  • Humans
  • Incidence
  • Male
  • Middle Aged
  • Neoplasms* / epidemiology
  • Neoplasms* / etiology
  • Risk Factors
  • Taiwan / epidemiology
  • Young Adult