Rapid response of lichen planus to baricitinib associated with suppression of cytotoxic CXCL13+CD8+ T cells

J Clin Invest. 2024 Nov 14;135(2):e179436. doi: 10.1172/JCI179436.

Abstract

BACKGROUNDCutaneous lichen planus (LP) is a recalcitrant, difficult-to-treat, inflammatory skin disease characterized by pruritic, flat-topped, violaceous papules on the skin. Baricitinib is an oral Janus kinase (JAK) 1/2 inhibitor that interrupts the signaling pathway of IFN-γ, a cytokine implicated in the pathogenesis of LP.METHODSIn this phase II trial, 12 patients with cutaneous LP received 2 mg daily baricitinib for 16 weeks, accompanied by in-depth spatial, single-cell, and bulk transcriptomic profiling of pre- and posttreatment samples.RESULTSAn early and sustained clinical response was seen, with 83.3% of patients responsive at week 16. Our molecular data identified a unique, oligoclonal IFN-γ, CD8+, and CXCL13+ cytotoxic T cell population in LP skin and demonstrated a rapid decrease in IFN signature within 2 weeks of treatment, most prominently in the basal layer of the epidermis.CONCLUSIONThis study demonstrates the efficacy and molecular mechanisms of JAK inhibition in LP.TRIAL REGISTRATIONNCT05188521FUNDINGEli Lilly, Appignani Benefactor Funds, 5P30AR075043, Mayo Clinic Clinical Trials Stimulus Funds.

Keywords: Dermatology; Drug therapy; T cells; Th1 response.

Publication types

  • Clinical Trial, Phase II

MeSH terms

  • Adult
  • Aged
  • Azetidines* / administration & dosage
  • CD8-Positive T-Lymphocytes* / immunology
  • CD8-Positive T-Lymphocytes* / pathology
  • Chemokine CXCL13* / immunology
  • Female
  • Humans
  • Interferon-gamma / immunology
  • Janus Kinase Inhibitors*
  • Lichen Planus* / drug therapy
  • Lichen Planus* / immunology
  • Lichen Planus* / pathology
  • Male
  • Middle Aged
  • Purines
  • Pyrazoles* / administration & dosage
  • Sulfonamides* / administration & dosage

Substances

  • baricitinib
  • Azetidines
  • Purines
  • Sulfonamides
  • Pyrazoles
  • Chemokine CXCL13
  • Interferon-gamma
  • Janus Kinase Inhibitors