A family with congenital suprabulbar paresis (Worster-Drought syndrome)

Clin Genet. 1986 Feb;29(2):147-50. doi: 10.1111/j.1399-0004.1986.tb01239.x.


A three generation family is described in which four members were found to have congenital suprabulbar paresis (Worster-Drought syndrome). It is suggested that some cases of congenital suprabulbar paresis are inherited as an autosomal dominant trait with variable expression and penetrance.

Publication types

  • Case Reports

MeSH terms

  • Bulbar Palsy, Progressive / congenital*
  • Bulbar Palsy, Progressive / genetics
  • Bulbar Palsy, Progressive / physiopathology
  • Child
  • Dysarthria / genetics
  • Facial Muscles / physiopathology
  • Humans
  • Intellectual Disability / genetics
  • Male
  • Mouth
  • Palate
  • Pedigree
  • Syndrome
  • Tongue