Bilateral papillary cystadenoma of the epididymis as a component of von Hippel-Lindau's syndrome: report of a case presenting as infertility

J Urol. 1985 Feb;133(2):288-9. doi: 10.1016/s0022-5347(17)48920-8.


We report a case of bilateral papillary cystadenoma of the epididymis thought to be a component of the von Hippel-Lindau syndrome. The patient was hospitalized initially because of infertility. He had undergone a craniotomy 2 years previously for the diagnosis of a cerebellar hemangioblastoma. Funduscopy had revealed angiomatous lesions of the left eye. The von Hippel-Lindau syndrome is discussed briefly and the importance of long-term urological followup for possible presentation of silent renal carcinoma is emphasized. Patients with bilateral epididymal papillary cystadenoma are prone to have other components of the von Hippel-Lindau syndrome, and clinical studies are indicated in all such patients.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Angiomatosis / complications*
  • Cystadenoma / complications*
  • Cystadenoma / pathology
  • Epididymis*
  • Humans
  • Infertility, Male / etiology*
  • Male
  • Testicular Neoplasms / complications*
  • Testicular Neoplasms / pathology
  • von Hippel-Lindau Disease / complications*
  • von Hippel-Lindau Disease / pathology