Absent Pericardium Causing Extreme Levoposition in a Child

Clin Case Rep. 2025 Jan 2;13(1):e70047. doi: 10.1002/ccr3.70047. eCollection 2025 Jan.

Abstract

During surgical repair of congenital heart defects, surgeons often come across anomalies that might not have been adequately illustrated in preoperative imaging. In this case image, we describe the absence of pericardium which was discovered during surgical repair of a sinus venosus defect in a small child.

Keywords: absent pericardium; congenital heart disease; pericardial disease; sinus venosus.