Khdrbs1 drives re-differentiation of bipotential progenitor cells by inhibiting p53 in zebrafish biliary-mediated liver regeneration

Development. 2025 Feb 15;152(4):DEV204266. doi: 10.1242/dev.204266. Epub 2025 Feb 28.

Abstract

After severe liver injury, biliary epithelial cells (BECs) undergo de-differentiation into bipotential progenitor cells (BPPCs), which subsequently re-differentiate into nascent hepatocytes and BECs to accomplish liver regeneration. However, the crucial factors governing the re-differentiation process of BPPCs remain largely unknown. Here, using a zebrafish model of severe liver injury, we observed specific expression of khdrbs1a and khdrbs1b (collectively known as khdrbs1) in BPPCs through single-cell RNA analyses and fluorescence in situ hybridization. Subsequently, to eliminate the genetic compensation, we generated a CRISPR/dead Cas9-mediated system for interfering with khdrbs1 in BECs, which caused defective liver regeneration and impaired re-differentiation of BPPCs. Furthermore, the khdrbs1-/- mutant displayed impaired proliferation and re-differentiation of BPPCs during liver regeneration. Mechanistically, p53 signaling was activated in response to the loss of khdrbs1, and tp53 mutation partially rescued the defective liver regeneration of the khdrbs1-/- mutant. In summary, we conclude that Khdrbs1 promotes the re-differentiation of BPPCs in part by inhibiting p53 activation during biliary-mediated liver regeneration in zebrafish.

Keywords: Sam68; Biliary epithelial cell; Cell proliferation; Liver injury; Transdifferentiation.

MeSH terms

  • Animals
  • Biliary Tract* / cytology
  • Biliary Tract* / metabolism
  • Cell Differentiation* / genetics
  • Cell Proliferation / genetics
  • Epithelial Cells / cytology
  • Epithelial Cells / metabolism
  • Hepatocytes / cytology
  • Hepatocytes / metabolism
  • Liver / metabolism
  • Liver Regeneration* / genetics
  • Liver Regeneration* / physiology
  • Signal Transduction
  • Stem Cells* / cytology
  • Stem Cells* / metabolism
  • Tumor Suppressor Protein p53* / genetics
  • Tumor Suppressor Protein p53* / metabolism
  • Zebrafish Proteins* / genetics
  • Zebrafish Proteins* / metabolism
  • Zebrafish* / genetics
  • Zebrafish* / metabolism

Substances

  • Tumor Suppressor Protein p53
  • Zebrafish Proteins
  • tp53 protein, zebrafish