Cognate interaction-dependent pathogenicity of meningeal B cells drives neuroinflammation relapse

Immunity. 2025 Sep 9;58(9):2256-2270.e8. doi: 10.1016/j.immuni.2025.06.016. Epub 2025 Jul 15.

Abstract

B cells are central drivers of central nervous system (CNS) autoimmune disorders, including multiple sclerosis (MS). Although the brain meninges normally maintain a stringently non-self-reactive B cell repertoire, how disruption of this local immune tolerance contributes to pathology remains unclear. Here, we demonstrated that autoreactive B cells at the brain border accelerated neuroinflammation by directly engaging encephalitogenic T cells. Intracisterna magna injections, used to selectively manipulate meningeal B cell populations in the 2D2 transfer experimental autoimmune encephalomyelitis (EAE) model, revealed that autoreactive B-T interactions in the leptomeninges amplified a local pro-inflammatory loop, promoting neutrophil recruitment and endothelial activation before disease onset. This mechanism required major histocompatibility complex class II (MHC class II) expression by B cells and granulocyte-macrophage colony-stimulating factor (GM-CSF) production by T cells. Furthermore, targeted depletion of brain-localized B cells attenuated EAE relapses in a passive EAE model. These findings establish brain-localized autoreactive B cells as crucial initiators of neuroinflammation and promising therapeutic targets in relapsing MS.

Keywords: B cells; EAE; Endothelial cell; GM-CSF; antigen presentation; autoimmune disease; meninges; neuroinflammation; vascular inflammation.

MeSH terms

  • Animals
  • B-Lymphocytes* / immunology
  • Brain / immunology
  • Brain / pathology
  • Disease Models, Animal
  • Encephalomyelitis, Autoimmune, Experimental* / immunology
  • Encephalomyelitis, Autoimmune, Experimental* / pathology
  • Female
  • Granulocyte-Macrophage Colony-Stimulating Factor / metabolism
  • Histocompatibility Antigens Class II / immunology
  • Histocompatibility Antigens Class II / metabolism
  • Humans
  • Meninges* / immunology
  • Meninges* / pathology
  • Mice
  • Mice, Inbred C57BL
  • Multiple Sclerosis* / immunology
  • Neuroinflammatory Diseases* / immunology
  • Recurrence
  • T-Lymphocytes / immunology

Substances

  • Histocompatibility Antigens Class II
  • Granulocyte-Macrophage Colony-Stimulating Factor