Pulmonary Artery Stenting for Widespread Distal Congenital Stenoses

S Wiltshire; F Collins; E Kotlyar; K Kearney; E Lau; P Macdonald; D Boshell; R Cordina

doi:10.1016/j.jaccas.2025.105311

Pulmonary Artery Stenting for Widespread Distal Congenital Stenoses

JACC Case Rep. 2025 Oct 1;30(30):105311. doi: 10.1016/j.jaccas.2025.105311.

Authors

S Wiltshire¹, F Collins², E Kotlyar¹, K Kearney³, E Lau², P Macdonald¹, D Boshell¹, R Cordina⁴

Affiliations

¹ St Vincent's Hospital, Darlinghurst, Australia.
² Royal Prince Alfred Hospital, Camperdown, Australia.
³ UT Southwestern Medical Center, Dallas, Texas, USA.
⁴ Royal Prince Alfred Hospital, Camperdown, Australia. Electronic address: Rachael.cordina@sydney.edu.au.

Abstract

Background: Pulmonary artery stenting is rarely reported in adults with distal and widespread congenital pulmonary artery stenoses or hypoplasia.

Case summary: A 35-year-old woman with diffuse distal congenital pulmonary artery hypoplasia and symptomatic right heart failure underwent pulmonary artery stenting, experiencing significant clinical improvement. A 62-year-old woman with widespread distal pulmonary artery stenoses underwent stenting owing to symptomatic nonsustained ventricular tachycardia and poor right ventricular contractile reserve. Her arrhythmia resolved and she experienced improvement of right ventricular contractile reserve. Both patients have an elastin gene mutation.

Discussion: There are limited reports of percutaneous intervention for adults with distal and widespread pulmonary artery stenoses or hypoplasia. We describe 2 successful cases of pulmonary artery stenting in this population.

Take-home message: Distal and widespread congenital pulmonary artery stenoses or hypoplasia can be treated with stenting when performed in well-selected patients by an experienced proceduralist in the right clinical setting.

Keywords: pulmonary circulation; stenosis; stents.

Publication types

Case Reports