A Phase I Trial of Nab-Paclitaxel in Combination With Gemcitabine for Relapsed/Refractory Pediatric Solid Tumors

Pediatr Blood Cancer. 2026 Jan;73(1):e32102. doi: 10.1002/pbc.32102. Epub 2025 Oct 14.

Abstract

Background: The single-agent pediatric maximum tolerated dose (MTD) of nab-paclitaxel is significantly higher than adult dosing. We conducted a Phase I trial to establish the MTD/recommended Phase 2 dose (RP2D) of nab-paclitaxel with gemcitabine in children with relapsed/refractory solid tumors.

Methods: Nab-paclitaxel was administered intravenously with fixed-dose gemcitabine on days 1, 8, and 15 of 28-day cycles. Three dose levels (DL) of nab-paclitaxel, 180, 210, and 240 mg/m2, were evaluated using a rolling six design. Toxicity, nab-paclitaxel pharmacokinetics (PK), and radiologic responses were evaluated. Pretreatment tumor tissue was assessed for SPARC and CAV-1.

Results: Twenty-four patients enrolled, 22 received therapy, and 20 were evaluable for dose-limiting toxicity (DLT): 17 during dose escalation and 3 in dose expansion at the MTD. Median age was 12.5 years. Diagnoses included osteosarcoma (n = 11), neuroblastoma (n = 4), and rhabdomyosarcoma (n = 4). At the starting dose level (gemcitabine 1000 mg/m2, nab-paclitaxel 180 mg/m2), two of five patients experienced DLT, prompting an amendment lowering gemcitabine to 675 mg/m2/dose. Post-amendment, nab-paclitaxel 240 mg/m2/dose with gemcitabine 675 mg/m2/dose was identified as the MTD. Grade ≥3 hematologic toxicities were common. Two patients experienced a partial response (Wilms tumor and osteosarcoma), and PK exhibited linearity across DL. SPARC immunoreactivity was present in most tumors, while CAV-1 immunoreactivity was infrequent.

Conclusions: The MTD/RP2D of nab-paclitaxel with gemcitabine in patients with relapsed/refractory pediatric solid tumors is nab-paclitaxel 240 mg/m2/dose and gemcitabine 675 mg/m2/dose on days 1, 8, and 15 of 28-day cycles; responses were limited in this patient population.

Keywords: Phase I; gemcitabine; nab‐paclitaxel; pediatric; solid tumor.

Publication types

  • Clinical Trial, Phase I

MeSH terms

  • Adolescent
  • Albumins / administration & dosage
  • Albumins / adverse effects
  • Albumins / pharmacokinetics
  • Antineoplastic Combined Chemotherapy Protocols* / administration & dosage
  • Antineoplastic Combined Chemotherapy Protocols* / adverse effects
  • Antineoplastic Combined Chemotherapy Protocols* / pharmacokinetics
  • Bone Neoplasms / drug therapy
  • Child
  • Child, Preschool
  • Deoxycytidine / administration & dosage
  • Deoxycytidine / adverse effects
  • Deoxycytidine / analogs & derivatives
  • Drug Resistance, Neoplasm
  • Female
  • Follow-Up Studies
  • Gemcitabine
  • Humans
  • Male
  • Maximum Tolerated Dose
  • Neoplasm Recurrence, Local* / drug therapy
  • Neoplasm Recurrence, Local* / pathology
  • Neoplasms* / drug therapy
  • Neoplasms* / pathology
  • Neuroblastoma* / drug therapy
  • Neuroblastoma* / pathology
  • Osteonectin / metabolism
  • Osteosarcoma* / drug therapy
  • Osteosarcoma* / pathology
  • Paclitaxel / administration & dosage
  • Paclitaxel / adverse effects
  • Prognosis
  • Rhabdomyosarcoma* / drug therapy
  • Rhabdomyosarcoma* / pathology

Substances

  • 130-nm albumin-bound paclitaxel
  • Albumins
  • Deoxycytidine
  • Gemcitabine
  • Osteonectin
  • Paclitaxel