Early lesion of Pelizaeus-Merzbacher disease: electron microscopic and biochemical study

J Neuropathol Exp Neurol. 1973 Apr;32(2):313-33. doi: 10.1097/00005072-197304000-00010.
No abstract available

MeSH terms

  • Autopsy
  • Brain / pathology*
  • Brain Chemistry
  • Cathepsins / metabolism
  • Cerebrosides / metabolism
  • Chromatography, Thin Layer
  • Cytoplasm
  • Diffuse Cerebral Sclerosis of Schilder / enzymology
  • Diffuse Cerebral Sclerosis of Schilder / genetics
  • Diffuse Cerebral Sclerosis of Schilder / metabolism*
  • Diffuse Cerebral Sclerosis of Schilder / pathology
  • Esterases / metabolism
  • Humans
  • Hydrolases / metabolism
  • Inclusion Bodies
  • Infant
  • Macrophages
  • Male
  • Microscopy, Electron
  • Myelin Sheath
  • Nerve Tissue Proteins / metabolism
  • Neuroglia
  • Pedigree
  • Staining and Labeling
  • Subcellular Fractions
  • Sulfoglycosphingolipids / metabolism

Substances

  • Cerebrosides
  • Nerve Tissue Proteins
  • Sulfoglycosphingolipids
  • Hydrolases
  • Esterases
  • Cathepsins