Pediatric and Familial Genetic Arrhythmia Syndromes: Evaluation of Bidirectional Ventricular Tachycardia-Differential Diagnosis

Heart Fail Clin. 2026 Jan;22(1):89-96. doi: 10.1016/j.hfc.2025.09.003.

Abstract

Bidirectional ventricular tachycardia is a unique arrhythmia that can herald lethal arrhythmia syndromes. Using cases based on real patient stories, this article examines 3 different presentations to help clinicians learn the differential diagnosis associated with this condition. Each associated genetic disorder will be briefly discussed, and valuable tips for distinguishing them from each other will be provided.

Keywords: Anderson-Tawil syndrome; Bidirectional; CPVT; TECRL; Ventricular tachycardia.

Publication types

  • Review
  • Case Reports

MeSH terms

  • Arrhythmias, Cardiac* / diagnosis
  • Arrhythmias, Cardiac* / genetics
  • Arrhythmias, Cardiac* / physiopathology
  • Child
  • Diagnosis, Differential
  • Electrocardiography
  • Female
  • Humans
  • Male
  • Tachycardia
  • Tachycardia, Ventricular* / diagnosis
  • Tachycardia, Ventricular* / genetics

Supplementary concepts

  • Bidirectional tachycardia