We report the case of an immunocompromised patient with previously unrecognized Mendelian susceptibility to mycobacterial disease due to interleukin-12Rβ1 deficit, who developed fatal disseminated Mycobacterium tilburgii infection. Mycobacterial invasion caused severe neurologic complications, including refractory status epilepticus, leading to death, despite therapies, including surgical interventions.
Keywords: Fatal infection; IL12Rβ1 deficit; Mendelian susceptibility to mycobacterial disease; Mycobacterium tilburgii.
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