Cofilin-1 is a redox-sensitive guard of the NLRP3 inflammasome

Nat Immunol. 2026 May;27(5):937-948. doi: 10.1038/s41590-026-02477-8. Epub 2026 Mar 18.

Abstract

Mutations in NLRP3 can cause a spectrum of the autoinflammatory cryopyrin-associated periodic syndromes (CAPS). Reactive oxygen species (ROS) have a central role in NLRP3 inflammasome activation. Here we show that cofilin-1, an actin-severing protein, is a negative regulator of the NLRP3 inflammasome. In resting cells, cofilin-1 directly bound NLRP3, but after stimulation with NLRP3 inflammasome activators, it was oxidized by ROS and dissociated from NLRP3. CAPS-associated mutant NLRP3 exhibited reduced binding to cofilin-1. Residues 101-104 of cofilin-1 were critical for NLRP3 interaction. Oxidation-independent peptides containing this NLRP3 binding motif suppressed inflammasome activation induced by endogenous CAPS-associated mutations and ex vivo NLRP3 activators such as ATP and nigericin. Bioinformatic structural analyses corroborate a model in which cofilin-1 has a pivotal function in NLRP3 activation by ROS and support the potential use of cofilin-1-derived peptides in individuals who are unresponsive to or intolerant of other forms of NLRP3 blockade.

MeSH terms

  • Animals
  • Cofilin 1* / chemistry
  • Cofilin 1* / genetics
  • Cofilin 1* / immunology
  • Cofilin 1* / metabolism
  • Cryopyrin-Associated Periodic Syndromes* / genetics
  • Cryopyrin-Associated Periodic Syndromes* / immunology
  • Cryopyrin-Associated Periodic Syndromes* / metabolism
  • HEK293 Cells
  • Humans
  • Inflammasomes* / immunology
  • Inflammasomes* / metabolism
  • Mice
  • Mutation
  • NLR Family, Pyrin Domain-Containing 3 Protein* / genetics
  • NLR Family, Pyrin Domain-Containing 3 Protein* / metabolism
  • Oxidation-Reduction
  • Protein Binding
  • Reactive Oxygen Species / metabolism

Substances

  • NLR Family, Pyrin Domain-Containing 3 Protein
  • Inflammasomes
  • Reactive Oxygen Species
  • Cofilin 1
  • NLRP3 protein, human