Chronic neutropenia and abnormal cellular immunity in cartilage-hair hypoplasia

N Engl J Med. 1970 Jan 29;282(5):231-6. doi: 10.1056/NEJM197001292820501.
No abstract available

MeSH terms

  • Abnormalities, Multiple / complications
  • Adolescent
  • Agranulocytosis / complications*
  • Antibody Formation
  • Bone and Bones / abnormalities
  • Cartilage Diseases / congenital*
  • Chickenpox / complications
  • Child
  • Child, Preschool
  • Chronic Disease
  • Dwarfism / diagnostic imaging
  • Dwarfism / immunology*
  • Female
  • Hair* / pathology
  • Humans
  • Hypersensitivity, Delayed
  • Immunologic Deficiency Syndromes*
  • In Vitro Techniques
  • Lectins / pharmacology
  • Leukocyte Count
  • Lymphocyte Activation
  • Lymphocytes / immunology
  • Lymphopenia / immunology
  • Male
  • Radiography
  • Respiratory Tract Infections / complications
  • Saliva / immunology
  • Skin Tests
  • Skin Transplantation
  • Transplantation Immunology
  • Transplantation, Homologous
  • gamma-Globulins / analysis

Substances

  • Lectins
  • gamma-Globulins