Decompression with or without Duraplasty for Chiari I and Syringomyelia

N Engl J Med. 2026 May 28;394(20):2015-2025. doi: 10.1056/NEJMoa2402821.

Abstract

Background: In children with Chiari type I malformation and syringomyelia, neurosurgical posterior fossa decompression (PFD) provides clinical improvement, but whether duraplasty (incising the dura and placing a dural graft) improves outcomes is unclear.

Methods: We conducted a multicenter, cluster-randomized, controlled trial of PFD with duraplasty (PFD-D) as compared with PFD alone. Persons 21 years of age or younger with cerebellar tonsillar ectopia of at least 5 mm and a maximum syrinx diameter of 3.0 to 9.9 mm were enrolled at 38 centers. Centers were cluster-randomized: all the participants within each center underwent the same intervention. The primary outcome was surgical complications within 6 months. Secondary outcomes were clinical improvement, syrinx reduction, and repeat decompression at 10 to 24 months and the change in overall health-related quality of life at 6 to 24 months.

Results: A total of 162 participants were included in the trial, of whom 78 were assigned to undergo PFD-D and 84 to undergo PFD alone. The percentage of participants with complications within 6 months was 14% with PFD-D and 6% with PFD (adjusted odds ratio, 2.59; 95% confidence interval [CI], 0.86 to 7.84; P = 0.11). At 24 months, the percentage of participants with clinical improvement was 58% with PFD-D and 46% with PFD; the mean (±SD) syrinx reduction was 3.08±2.33 mm and 1.22±1.79 mm, respectively; and the percentage of participants with repeat decompression was 3% and 14%. Changes in health-related quality of life were similar in the two groups.

Conclusions: The percentage of participants with surgical complications did not differ significantly between those who underwent PFD-D and and those who underwent PFD alone. Larger trials are needed to determine the relative benefits and risks of these two procedures. (Funded by the Patient-Centered Outcomes Research Institute and others; ClinicalTrials.gov number, NCT02669836.).

Publication types

  • Multicenter Study
  • Randomized Controlled Trial
  • Comparative Study

MeSH terms

  • Adolescent
  • Arnold-Chiari Malformation* / complications
  • Arnold-Chiari Malformation* / diagnostic imaging
  • Arnold-Chiari Malformation* / psychology
  • Arnold-Chiari Malformation* / surgery
  • Cervical Vertebrae
  • Child
  • Child, Preschool
  • Cranial Fossa, Posterior / surgery
  • Decompression, Surgical* / adverse effects
  • Decompression, Surgical* / methods
  • Dura Mater* / surgery
  • Dura Mater* / transplantation
  • Female
  • Follow-Up Studies
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Postoperative Complications* / epidemiology
  • Quality of Life
  • Reoperation
  • Spinal Cord / diagnostic imaging
  • Spinal Cord / surgery
  • Syringomyelia* / complications
  • Syringomyelia* / diagnostic imaging
  • Syringomyelia* / psychology
  • Syringomyelia* / surgery
  • Treatment Outcome

Associated data

  • ClinicalTrials.gov/NCT02669836