"Ragged-red" fibers in Leigh's disease

Neurology. 1974 Jan;24(1):49-54. doi: 10.1212/wnl.24.1.49.
No abstract available

MeSH terms

  • Adenosine Triphosphatases / metabolism
  • Autopsy
  • Brain Stem / pathology*
  • Cerebellum / pathology
  • Cerebral Cortex / pathology
  • Child
  • Encephalomalacia / pathology*
  • Gliosis
  • Humans
  • Intellectual Disability / pathology
  • Male
  • Microscopy, Electron
  • Mitochondria, Muscle / enzymology
  • Muscles / enzymology
  • Muscles / pathology*
  • Pons / pathology
  • Psychomotor Disorders / pathology
  • Succinate Dehydrogenase / metabolism
  • Tegmentum Mesencephali / pathology

Substances

  • Succinate Dehydrogenase
  • Adenosine Triphosphatases