Glucose-6-phosphatase deficiency and hyperlipaemia

Clin Chim Acta. 1970 Dec;30(3):775-8. doi: 10.1016/0009-8981(70)90274-3.
No abstract available

MeSH terms

  • Adenoma, Islet Cell / metabolism
  • Biopsy
  • Blood Glucose / metabolism
  • Carbon Isotopes
  • Child, Preschool
  • Citrates / metabolism
  • Coenzyme A / metabolism
  • Fatty Acids / biosynthesis
  • Female
  • Glycogen Storage Disease / metabolism
  • Glycogen Storage Disease Type I / complications
  • Glycogen Storage Disease Type I / metabolism*
  • Glycoside Hydrolases / metabolism
  • Humans
  • Hyperlipidemias / etiology
  • Infant
  • Insulin / blood
  • Lactates / blood
  • Liver / metabolism*
  • Malonates / metabolism

Substances

  • Blood Glucose
  • Carbon Isotopes
  • Citrates
  • Fatty Acids
  • Insulin
  • Lactates
  • Malonates
  • Glycoside Hydrolases
  • Coenzyme A