No abstract available
MeSH terms
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Adenoma, Islet Cell / metabolism
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Biopsy
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Blood Glucose / metabolism
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Carbon Isotopes
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Child, Preschool
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Citrates / metabolism
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Coenzyme A / metabolism
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Fatty Acids / biosynthesis
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Female
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Glycogen Storage Disease / metabolism
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Glycogen Storage Disease Type I / complications
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Glycogen Storage Disease Type I / metabolism*
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Glycoside Hydrolases / metabolism
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Humans
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Hyperlipidemias / etiology
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Infant
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Insulin / blood
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Lactates / blood
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Liver / metabolism*
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Malonates / metabolism
Substances
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Blood Glucose
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Carbon Isotopes
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Citrates
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Fatty Acids
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Insulin
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Lactates
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Malonates
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Glycoside Hydrolases
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Coenzyme A