Erythropoietic protoporphyria. A clinical study based on 29 cases in 14 families

Arch Dermatol. 1974 Jul;110(1):58-64. doi: 10.1001/archderm.110.1.58.
No abstract available

MeSH terms

  • Adolescent
  • Adult
  • Age Factors
  • Aged
  • Biopsy
  • Child
  • Child, Preschool
  • Cholelithiasis / complications
  • Erythrocytes / metabolism*
  • Feces / analysis
  • Female
  • Genes
  • Hemoglobins / analysis
  • Humans
  • Hydroxychloroquine / administration & dosage
  • Infant
  • Iron / blood
  • Liver / pathology
  • Liver Function Tests
  • Male
  • Middle Aged
  • Nails / pathology
  • Pedigree
  • Porphyrias / genetics*
  • Porphyrias / pathology
  • Porphyrias / therapy
  • Porphyrins / analysis
  • Porphyrins / metabolism*
  • Pregnancy
  • Remission, Spontaneous
  • Skin / pathology
  • Spectrum Analysis
  • Steroids / administration & dosage
  • Transferrin / analysis

Substances

  • Hemoglobins
  • Porphyrins
  • Steroids
  • Transferrin
  • Hydroxychloroquine
  • Iron