No abstract available
Publication types
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Research Support, Non-U.S. Gov't
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Review
MeSH terms
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Chemical Phenomena
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Chemistry
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Child, Preschool
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Glucan 1,4-alpha-Glucosidase / deficiency
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Glucosephosphate Dehydrogenase Deficiency / metabolism
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Glucosephosphate Dehydrogenase Deficiency / pathology
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Glycogen / metabolism*
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Glycogen Debranching Enzyme System / deficiency
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Glycogen Storage Disease / enzymology*
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Glycogen Storage Disease / pathology
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Humans
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Liver / ultrastructure
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Liver Glycogen / metabolism
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Male
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Phosphorylases / deficiency
Substances
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Glycogen Debranching Enzyme System
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Liver Glycogen
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Glycogen
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Phosphorylases
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Glucan 1,4-alpha-Glucosidase