The glycogen storage diseases

J Clin Pathol Suppl (R Coll Pathol). 1974:8:106-21.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Chemical Phenomena
  • Chemistry
  • Child, Preschool
  • Glucan 1,4-alpha-Glucosidase / deficiency
  • Glucosephosphate Dehydrogenase Deficiency / metabolism
  • Glucosephosphate Dehydrogenase Deficiency / pathology
  • Glycogen / metabolism*
  • Glycogen Debranching Enzyme System / deficiency
  • Glycogen Storage Disease / enzymology*
  • Glycogen Storage Disease / pathology
  • Humans
  • Liver / ultrastructure
  • Liver Glycogen / metabolism
  • Male
  • Phosphorylases / deficiency

Substances

  • Glycogen Debranching Enzyme System
  • Liver Glycogen
  • Glycogen
  • Phosphorylases
  • Glucan 1,4-alpha-Glucosidase