Urinary mannose in mannosidosis

J Pediatr. 1973 Apr;82(4):686-8. doi: 10.1016/s0022-3476(73)80599-2.
No abstract available

MeSH terms

  • Acid Phosphatase / analysis
  • Carbohydrate Metabolism, Inborn Errors / complications
  • Carbohydrate Metabolism, Inborn Errors / urine*
  • Child
  • Child, Preschool
  • Chromatography
  • Female
  • Galactosidases / analysis
  • Glucosidases / analysis
  • Glucuronidase / analysis
  • Glycoside Hydrolases / analysis
  • Hexosaminidases / analysis
  • Humans
  • Liver / enzymology
  • Lysosomes / enzymology*
  • Mannose / metabolism*
  • Monosaccharides / urine
  • Mucopolysaccharidoses / etiology

Substances

  • Monosaccharides
  • Acid Phosphatase
  • Galactosidases
  • Glucosidases
  • Glycoside Hydrolases
  • Hexosaminidases
  • Glucuronidase
  • Mannose