Effects of maple syrup urine disease metabolites on mouse L-fibroblasts in vitro: a fine structural and biochemical study

J Neurochem. 1974 Jun;22(6):957-64. doi: 10.1111/j.1471-4159.1974.tb04322.x.
No abstract available

Publication types

  • Comparative Study

MeSH terms

  • Animals
  • Caprylates / pharmacology*
  • Carbon Radioisotopes
  • Cell Count
  • Cell Division / drug effects
  • Chromatography, Thin Layer
  • Humans
  • Hydrogen-Ion Concentration
  • Isoleucine / metabolism
  • Isoleucine / pharmacology*
  • Keto Acids / metabolism
  • Keto Acids / pharmacology*
  • L Cells / cytology
  • L Cells / drug effects
  • L Cells / metabolism*
  • Leucine / pharmacology*
  • Maple Syrup Urine Disease / blood*
  • Mice
  • Microscopy, Electron
  • Time Factors
  • Tritium
  • Valerates / metabolism
  • Valerates / pharmacology*

Substances

  • Caprylates
  • Carbon Radioisotopes
  • Keto Acids
  • Valerates
  • Isoleucine
  • Tritium
  • Leucine