Leigh's encephalomyelopathy: an inborn error of gluconeogenesis

Arch Dis Child. 1968 Aug;43(230):423-6. doi: 10.1136/adc.43.230.423.
No abstract available

MeSH terms

  • Animals
  • Blood Glucose / analysis
  • Brain Diseases / etiology*
  • Carbohydrate Metabolism, Inborn Errors / complications*
  • Carboxy-Lyases / metabolism
  • Epinephrine / pharmacology
  • Glucagon / metabolism
  • Gluconeogenesis*
  • Glucose Tolerance Test
  • Humans
  • Infant
  • Lactates / blood
  • Liver / enzymology
  • Male
  • Phosphotransferases / metabolism
  • Pyruvates / blood
  • Rats
  • Thioctic Acid / therapeutic use

Substances

  • Blood Glucose
  • Lactates
  • Pyruvates
  • Thioctic Acid
  • Glucagon
  • Phosphotransferases
  • Carboxy-Lyases
  • Epinephrine