Abstract
A review of cases indicated that gingival fibromatosis occurs in a variety of genetic entities. High risk for epilepsy and oligophrenia is associated if hypertrichosis is present. Other entities are symmetrical gingival fibromatosis; Zimmermann-Laband syndrome with bone, ear, nose and nail defects and hepatosplenomegaly; Murray syndrome with multiple hyaline dermal tumors; Rutherfurd syndrome with corneal dystrophy; Cowden syndrome with hypertrichosis, oligophrenia and giant fibroadenomatosis of breasts and Cross syndrome of hypopigmentation, oligophrenia and athetosis.
MeSH terms
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Abnormalities, Multiple / complications
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Adenofibroma / complications
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Albinism / complications
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Anodontia / genetics
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Athetosis / complications
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Bone and Bones / abnormalities
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Breast Neoplasms / complications
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Corneal Dystrophies, Hereditary / genetics
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Ear, External / abnormalities
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Epilepsy / complications
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Female
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Fibroma / complications
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Fibromatosis, Gingival / classification
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Fibromatosis, Gingival / genetics*
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Gingival Hypertrophy / genetics
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Hepatomegaly / complications
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Humans
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Hypertrichosis / complications
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Intellectual Disability / complications
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Jaw Abnormalities / complications
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Male
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Microphthalmos / complications
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Nails, Malformed / complications
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Nose Deformities, Acquired
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Splenomegaly / complications