Isolation and identification of methylcitrate, a major metabolic product of propionate in patients with propionic acidemia

MeSH terms

• Acids / urine
• Carbon Isotopes
• Chromatography
• Chromatography, Gas
• Chromatography, Paper
• Citrates / chemical synthesis
• Citrates / isolation & purification
• Citrates / urine*
• Coenzyme A / metabolism
• Humans
• Malonates / urine
• Mass Spectrometry
• Metabolism, Inborn Errors / etiology
• Metabolism, Inborn Errors / urine*
• Oxaloacetates / metabolism
• Propionates / blood*
• Propionates / metabolism