Ketotic hypoglycaemia associated with transient branched-chain aminoacidemia

Acta Paediatr Scand. 1972 Jan;61(1):81-9. doi: 10.1111/j.1651-2227.1972.tb15906.x.
No abstract available

Publication types

  • Case Reports

MeSH terms

  • Amino Acid Metabolism, Inborn Errors / diagnosis*
  • Amino Acids / blood
  • Amino Acids / cerebrospinal fluid
  • Birth Weight
  • Blood Glucose / analysis
  • Child
  • Child, Preschool
  • Creatinine / urine
  • Diet Therapy
  • Female
  • Growth Hormone / blood
  • Humans
  • Hypoglycemia / diagnosis*
  • Isoleucine / blood
  • Keto Acids / urine
  • Leucine / blood
  • Male
  • Maple Syrup Urine Disease / diagnosis*
  • Pre-Eclampsia / complications
  • Pregnancy
  • Valine / blood

Substances

  • Amino Acids
  • Blood Glucose
  • Keto Acids
  • Isoleucine
  • Growth Hormone
  • Creatinine
  • Leucine
  • Valine