Unilateral complete aplasia of the inner ear with associated tracheoesophageal fistula: report of a case

Otolaryngol Head Neck Surg (1979). 1979 Jul-Aug;87(4):435-9. doi: 10.1177/019459987908700407.


A case of unilateral complete aplasia of the petrous apex and inner ear associated with H-type tracheoesophageal fistula is reported. polytomography, computerized axial tomography, and plain film radiography confirmed the presence of this rare variant of inner ear aplasia. This patient, who has normal facial nerve function, is, to our knowledge, the first reported case of a nonthalidomide, Michel-type aplasia since the original report of Michel more than a century ago. Unilateral complete inner ear aplasia associated with tracheoesophageal fistula has not been previously reported.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Ear, Inner / abnormalities*
  • Ear, Inner / diagnostic imaging
  • Ear, Inner / embryology
  • Female
  • Humans
  • Petrous Bone / abnormalities
  • Petrous Bone / diagnostic imaging
  • Tomography, X-Ray
  • Tomography, X-Ray Computed
  • Tracheoesophageal Fistula / congenital*