Nigro-spino-dentatal degeneration with nuclear ophthalmoplegia. A unique and partially treatable clinico-pathological entity

J Neurol Sci. 1972 Oct;17(2):149-66. doi: 10.1016/0022-510x(72)90137-2.
No abstract available

MeSH terms

  • Adult
  • Aged
  • Ataxia / complications*
  • Ataxia / genetics
  • Ataxia / pathology
  • Basal Ganglia Diseases / complications
  • Basal Ganglia Diseases / genetics
  • Cerebellar Diseases / complications*
  • Cerebellar Diseases / genetics
  • Cerebellar Diseases / pathology
  • Cerebellar Nuclei / pathology
  • Female
  • Genes, Dominant
  • Humans
  • Male
  • Middle Aged
  • Nerve Degeneration*
  • Oculomotor Nerve / pathology
  • Ophthalmoplegia / complications*
  • Ophthalmoplegia / genetics
  • Ophthalmoplegia / pathology
  • Pedigree
  • Spinal Cord / pathology
  • Spinal Cord Diseases / complications*
  • Spinal Cord Diseases / genetics
  • Spinal Cord Diseases / pathology
  • Substantia Nigra / pathology
  • Tegmentum Mesencephali / pathology