Glutamine in the phenylketonuric central nervous system

N Engl J Med. 1970 Dec 17;283(25):1364-7. doi: 10.1056/NEJM197012172832503.
No abstract available

MeSH terms

  • Adolescent
  • Adult
  • Amino Acids / analysis
  • Amino Acids / blood
  • Amino Acids / cerebrospinal fluid
  • Biological Transport, Active
  • Brain / metabolism*
  • Brain Chemistry
  • Child
  • Female
  • Glutamine / analysis
  • Glutamine / blood
  • Glutamine / cerebrospinal fluid
  • Glutamine / metabolism*
  • Histidine / cerebrospinal fluid
  • Humans
  • Intellectual Disability / etiology
  • Intelligence Tests
  • Male
  • Middle Aged
  • Phenylketonurias / blood
  • Phenylketonurias / cerebrospinal fluid
  • Phenylketonurias / complications
  • Phenylketonurias / genetics
  • Phenylketonurias / metabolism*
  • Serine / cerebrospinal fluid
  • Threonine / cerebrospinal fluid
  • Tyrosine / analysis
  • Tyrosine / cerebrospinal fluid

Substances

  • Amino Acids
  • Glutamine
  • Threonine
  • Tyrosine
  • Serine
  • Histidine