Clinical observations of juvenile nonprogressive muscular atrophy localized in hand and forearm

J Neurol. 1976 Jan 14;211(2):105-10. doi: 10.1007/BF00313354.


Twenty-seven patients with juvenile nonprogressive muscular atrophy localized in the hand and forearm were analyzed. The clinical characteristics were juvenile male occurrence, insidious onset, specific distribution of localized muscular atrophy and a stationary course. On electromyography, denervation voltage (or giant NMU) is found in the atrophied muscles and sometimes in contralateral nonatrophied ones. Sensory disturbance was not remarkable. Although the etiological factor was not known, strenuous exercise of arms in sports was noted frequently in the history.

MeSH terms

  • Adolescent
  • Adult
  • Age Factors
  • Electromyography
  • Forearm*
  • Functional Laterality
  • Hand*
  • Humans
  • Lordosis
  • Male
  • Muscular Atrophy / diagnosis*
  • Muscular Atrophy / etiology
  • Muscular Atrophy / physiopathology
  • Physical Exertion
  • Reflex
  • Sensation