Urinary and cerebrospinal fluid oxypurine levels and allopurinol metabolism in the Lesch-Nyhan syndrome

Fed Proc. 1968 Jul-Aug;27(4):1055-9.
No abstract available

MeSH terms

  • Allopurinol / metabolism*
  • Chemistry, Clinical
  • Child
  • Child, Preschool
  • Chromatography, Gel
  • Chromatography, Ion Exchange
  • Humans
  • Hypoxanthines / cerebrospinal fluid*
  • Hypoxanthines / urine*
  • Purine-Pyrimidine Metabolism, Inborn Errors / cerebrospinal fluid*
  • Purine-Pyrimidine Metabolism, Inborn Errors / urine*
  • Transferases / metabolism
  • Uric Acid / blood
  • Uric Acid / urine
  • Xanthines / cerebrospinal fluid*
  • Xanthines / urine*

Substances

  • Hypoxanthines
  • Xanthines
  • Uric Acid
  • Allopurinol
  • Transferases