Increased non-protein-bound iron and decreased protection against superoxide-radical damage in cerebrospinal fluid from patients with neuronal ceroid lipofuscinoses

Lancet. 1982 Aug 28;2(8296):459-60. doi: 10.1016/s0140-6736(82)90492-5.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Age Factors
  • Central Nervous System Diseases / cerebrospinal fluid*
  • Ceroid / metabolism
  • Child
  • Child, Preschool
  • Free Radicals
  • Humans
  • Infant
  • Iron / cerebrospinal fluid*
  • Lipofuscin / metabolism*
  • Neurons
  • Oxidation-Reduction
  • Pigments, Biological / metabolism*
  • Protein Binding
  • Sphingolipidoses / cerebrospinal fluid*
  • Superoxides / cerebrospinal fluid

Substances

  • Ceroid
  • Free Radicals
  • Lipofuscin
  • Pigments, Biological
  • Superoxides
  • Iron