Evaluations of wasted mouse fibroblasts and SV-40 transformed human fibroblasts as models of ataxia telangiectasia in vitro

Mutat Res. 1984 Aug;140(4):219-22. doi: 10.1016/0165-7992(84)90081-2.

Abstract

Fibroblast cultures from wasted mice have been derived and the responses of these cultures to bleomycin treatment or gamma-irradiation have been examined. No differences were observed between wasted fibroblasts and littermate controls in the post-treatment inhibition of DNA replication. In contrast, a human SV-40 transformed ataxia telangiectasia fibroblast line mimicked the abnormal response of primary ataxia telangiectasia fibroblasts to gamma-rays or bleomycin and thus appears to be a useful in vitro model of ataxia telangiectasia.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Ataxia Telangiectasia / pathology*
  • Bleomycin / pharmacology
  • Cell Line
  • Cell Survival
  • Cell Transformation, Viral
  • DNA Replication / drug effects
  • DNA Replication / radiation effects
  • Disease Models, Animal*
  • Gamma Rays
  • Humans
  • Mice
  • Mice, Mutant Strains / physiology*
  • Simian virus 40

Substances

  • Bleomycin