Canine GM2-gangliosidosis: chemical and enzymatic features

Adv Exp Med Biol. 1984:174:431-40. doi: 10.1007/978-1-4684-1200-0_36.

Abstract

The chemical and enzymatic features in tissues of GM2-gangliosidosis are characterized by the analysis of glycolipids and FD-MS, and also by enzymatic analysis with DEAE-Sepharose column chromatography. The results suggest that canine GM2-gangliosidosis is equivalent to human juvenile GM2-gangliosidosis.

Publication types

  • Comparative Study

MeSH terms

  • Animals
  • Brain Chemistry*
  • Chromatography, Thin Layer
  • Dog Diseases / metabolism*
  • Dogs
  • G(M2) Ganglioside / metabolism*
  • Gangliosides / analysis*
  • Gangliosides / metabolism*
  • Gangliosidoses / metabolism
  • Gangliosidoses / veterinary*
  • Hexosaminidases / isolation & purification
  • Humans
  • Kidney / enzymology
  • Liver / analysis*
  • Mass Spectrometry
  • Sialic Acids / analysis
  • beta-N-Acetylhexosaminidases

Substances

  • Gangliosides
  • Sialic Acids
  • G(M2) Ganglioside
  • Hexosaminidases
  • beta-N-Acetylhexosaminidases