Abstract
The chemical and enzymatic features in tissues of GM2-gangliosidosis are characterized by the analysis of glycolipids and FD-MS, and also by enzymatic analysis with DEAE-Sepharose column chromatography. The results suggest that canine GM2-gangliosidosis is equivalent to human juvenile GM2-gangliosidosis.
MeSH terms
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Animals
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Brain Chemistry*
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Chromatography, Thin Layer
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Dog Diseases / metabolism*
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Dogs
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G(M2) Ganglioside / metabolism*
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Gangliosides / analysis*
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Gangliosides / metabolism*
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Gangliosidoses / metabolism
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Gangliosidoses / veterinary*
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Hexosaminidases / isolation & purification
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Humans
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Kidney / enzymology
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Liver / analysis*
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Mass Spectrometry
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Sialic Acids / analysis
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beta-N-Acetylhexosaminidases
Substances
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Gangliosides
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Sialic Acids
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G(M2) Ganglioside
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Hexosaminidases
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beta-N-Acetylhexosaminidases