The Moya-Moya syndrome: a report of two children

Clin Neurol Neurosurg. 1982;84(3):179-89. doi: 10.1016/0303-8467(82)90041-5.


Two patients with Moya-Moya syndrome are reported. The first patient has a trisomy 21 and is to our knowledge the third patient reported with the association of Down's syndrome and Moya-Moya. The second patient also demonstrates the typical Moya-Moya picture in angiography. Angiographic follow-up is demonstrated. The presenting age and symptoms, the symptoms in the course of the disease and the prognosis of 120 non-mongoloid cases of Moya-Moya are reviewed.

Publication types

  • Case Reports

MeSH terms

  • Arterial Occlusive Diseases / physiopathology*
  • Basilar Artery / diagnostic imaging
  • Carotid Arteries / diagnostic imaging
  • Cerebral Angiography
  • Child
  • Child, Preschool
  • Down Syndrome / complications
  • Humans
  • Male
  • Moyamoya Disease / complications
  • Moyamoya Disease / diagnostic imaging
  • Moyamoya Disease / physiopathology*