Von Recklinghausen's disease associated with gastrointestinal carcinoid tumors

Cancer. 1983 Jun 15;51(12):2206-8. doi: 10.1002/1097-0142(19830615)51:12<2206::aid-cncr2820511209>3.0.co;2-b.


The occurrence of both gastrointestinal carcinoid and von Recklinghausen's disease in the same patient is uncommon. There seems to be a predilection for ampullary carcinoids in these patients. This article reports the sixth case, including a review of the literature and a brief discussion of the implications of this finding. A carcinoid tumor should be suspected in any patient with von Recklinghausen's disease presenting with gastrointestinal bleeding, obstruction, abdominal pain, and particularly obstructive jaundice.

Publication types

  • Case Reports
  • Comparative Study
  • Review

MeSH terms

  • Ampulla of Vater
  • Carcinoid Tumor / complications*
  • Gastrointestinal Hemorrhage / etiology
  • Gastrointestinal Neoplasms / complications*
  • Humans
  • Intestinal Obstruction / etiology
  • Male
  • Middle Aged
  • Neurofibromatosis 1 / complications*
  • Pain / etiology