Genetic deficiencies of adenosine deaminase and purine nucleoside phosphorylase and their implications for therapy of leukemias

Curr Top Hematol. 1983:4:1-35.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.
  • Review

MeSH terms

  • Adenosine Deaminase / deficiency*
  • Adenosine Deaminase / genetics
  • Adenosine Deaminase / metabolism
  • Adenosine Deaminase Inhibitors
  • Animals
  • Child
  • Child, Preschool
  • Coformycin / adverse effects
  • Coformycin / analogs & derivatives
  • Coformycin / pharmacology
  • Coformycin / therapeutic use
  • Erythrocytes / enzymology
  • Female
  • Humans
  • Immunologic Deficiency Syndromes / enzymology
  • Leukemia / drug therapy*
  • Leukemia / enzymology
  • Male
  • Nucleoside Deaminases / deficiency*
  • Pentostatin
  • Pentosyltransferases / deficiency*
  • Purine-Nucleoside Phosphorylase / deficiency*
  • Transcobalamins / deficiency

Substances

  • Adenosine Deaminase Inhibitors
  • Transcobalamins
  • Coformycin
  • Pentostatin
  • Pentosyltransferases
  • Purine-Nucleoside Phosphorylase
  • Nucleoside Deaminases
  • Adenosine Deaminase