Two patients with posterior lenticonus; one was unilateral and the other was bilateral. The second patient had bilateral cataract extractions and the lenses were examined histopathologically. Postoperatively she did not have any amblyopia. The purpose of this presentation is to illustrate two points from the clinicopathological findings: The pathogenesis of the anomaly is mainly due to inherited thinning and weakness of the central part of the posterior lens capsule. We suggest that the posterior lenticonus without complicated cataract is not a main cause of profound amblyopia. The amblyopia is dependent on the age at which the cataract develops.