Long-term follow-up in the unoperated univentricular heart

Am J Cardiol. 1984 Apr 1;53(8):1124-8. doi: 10.1016/0002-9149(84)90648-9.


Type A univentricular heart is a severe congenital cardiac defect; 50% of patients are dead 14 years after diagnosis, a death rate of 4.8% per year. Type C univentricular heart is even more lethal; 50% of patients are dead 4 years after diagnosis. Pulmonary stenosis did not protect either group of patients in terms of overall survival. Of the patients in class I or II at initial diagnosis, 34% of patients with type A and 12% of those with type C were in class III or IV or had died at follow-up. The most common causes of death were dysrhythmia, congestive heart failure and sudden and unexplained death.

MeSH terms

  • Aged
  • Arrhythmias, Cardiac / mortality
  • Death, Sudden / etiology
  • Female
  • Follow-Up Studies
  • Heart Failure / mortality
  • Heart Ventricles / abnormalities*
  • Humans
  • Male
  • Mortality
  • Pulmonary Valve Stenosis / mortality