A 23 years old woman with the typical symptoms of Behçet's disease developed the psychopathological changes of an acute encephalitis which remitted after treatment with corticosteroids. 4 years later on appeared a Wallenberg-syndrome with pleocytosis. The symptomatology vanished nearly immediately after blood transfusion. Intercurrent the woman was delivered of a healthy boy. During the pregnancy the dosis of corticosteroids could be reduced. 10 years from the beginning of the first symptoms there exist more or less intensive stomatitis, vaginitis and inflammatory processes of the eyes despite corticosteroid therapy but no symptoms of the nervous system.