Moyamoya disease in children and its surgical treatment. Introduction of a new surgical procedure and its follow-up angiograms

Childs Brain. 1984;11(3):155-70. doi: 10.1159/000120172.


Moyamoya disease is an unusual form of chronic cerebrovascular occlusive disease characterized usually by bilateral stenosis of distal internal carotid arteries and their vicinity, by a hazy network of collateral circulation at the base of the brain called moyamoya vessels and clinically by recurring hemispheric ischemic attacks in children. This disease was first reported by a Japanese neurosurgeon and many reports and studies on this disease have been published in Japan. We report here the recent progress in the diagnosis of the disease and introduce a newly developed operative procedure which we think is an ideal surgical method for treating this disease in children.

MeSH terms

  • Anesthesia, General
  • Arterial Occlusive Diseases / surgery*
  • Cerebral Angiography
  • Cerebral Revascularization / methods*
  • Child
  • Electroencephalography
  • Follow-Up Studies
  • Humans
  • Moyamoya Disease / diagnosis
  • Moyamoya Disease / surgery*
  • Preanesthetic Medication
  • Scalp / blood supply
  • Tomography, X-Ray Computed