Fusion with enucleated fibroblasts corrects "I-cell" defect

Exp Cell Res. 1980 Jun;127(2):484-7. doi: 10.1016/0014-4827(80)90460-7.
No abstract available

MeSH terms

  • Cell Fusion
  • Cells, Cultured
  • Cytoplasm / physiology*
  • Fibroblasts
  • Gangliosidoses
  • Humans
  • Hybrid Cells / enzymology*
  • Hydrolases / metabolism*
  • Mannosidases / metabolism
  • Mucolipidoses / enzymology*
  • Mucolipidoses / pathology
  • beta-Galactosidase / metabolism

Substances

  • Hydrolases
  • Mannosidases
  • beta-Galactosidase