Sleep abnormalities in four cases of dyssynergia cerebellaris myoclonica of Ramsay-Hunt

Ital J Neurol Sci. 1981 May;2(2):159-63. doi: 10.1007/BF02335438.

Abstract

The nocturnal sleep of four patients with dyssynergia cerebellaris myoclonica (DCM) of Ramsay-Hunt was recorded with a polygraph. The following features were observed: a reduction of spindles, K complexes and vertex spikes; frequent arousals; rare rapid eye movements with a modification of their morphology and pattern; change in sleep stage percentages. In addition, myoclonus and polyspike-and-wave complexes appeared less frequently during sleep than during wakefulness. Three generalized convulsive and sixteen clonic seizures were recorded during stage 3/4 or on arousal. The clinical and physiopathological implications of these data are discussed.

MeSH terms

  • Adolescent
  • Cerebellar Ataxia / diagnosis*
  • Child
  • Electroencephalography
  • Epilepsies, Myoclonic / diagnosis
  • Epilepsy, Tonic-Clonic / diagnosis
  • Evoked Potentials
  • Female
  • Humans
  • Male
  • Myoclonic Cerebellar Dyssynergia / diagnosis*
  • Myoclonic Cerebellar Dyssynergia / genetics
  • Sleep Stages
  • Sleep Wake Disorders / diagnosis*