Cutaneous vasculitis in adult polymyositis/dermatomyositis

J Rheumatol. 1983 Feb;10(1):85-9.

Abstract

Seven (9.2%) of 76 patients with adult-onset polymyositis/dermatomyositis (PM/DM) seen over an 11-year period had cutaneous vasculitis. This was manifest by dermal and/or subcutaneous nodules in 4, periungual infarcts in 3 and digital ulceration in 2. When these 7 patients were compared to the remaining 69, a significant association was noted between cutaneous vasculitis and DM (p = .025); only 1 of 31 patients with primary PM and none of 18 with overlap syndromes had vasculitis. Furthermore, 2 (28.6%) of those with vasculitis had an associated malignancy compared to only 4 (5.8%) of those without vasculitis. These data document the occurrence of cutaneous vasculitis in adult-onset PM/DM and suggest that its presence may be a marker of an underlying malignancy.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adult
  • Dermatomyositis / complications*
  • Dermatomyositis / diagnosis
  • Female
  • Humans
  • Male
  • Middle Aged
  • Myositis / complications*
  • Myositis / diagnosis
  • Skin / blood supply
  • Skin Diseases / complications
  • Vasculitis / complications*
  • Vasculitis / diagnosis