High-performance liquid chromatographic separation of six essential amino acids and its use as an aid in the diagnosis of branched-chain ketoaciduria

J Chromatogr. 1982 Feb 12;227(2):497-502. doi: 10.1016/s0378-4347(00)80403-x.
No abstract available

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Amino Acid Metabolism, Inborn Errors / blood*
  • Amino Acid Metabolism, Inborn Errors / therapy
  • Amino Acid Metabolism, Inborn Errors / urine
  • Amino Acids, Essential / blood*
  • Chromatography, High Pressure Liquid / methods
  • Female
  • Humans
  • Infant, Newborn
  • Isoleucine / blood
  • Keto Acids / urine
  • Leucine / blood
  • Peritoneal Dialysis
  • Phenylalanine / blood
  • Time Factors
  • Valine / blood

Substances

  • Amino Acids, Essential
  • Keto Acids
  • Isoleucine
  • Phenylalanine
  • Leucine
  • Valine